2-year-old female child who presented with complaints of pain in abdomen for 3 days and 2 episodes of nonbilious vomiting. A vague mass was palpable just below umbilicus with ill-defined margins and firm surface. Ultrasonography whole abdomen was performed, and there was evidence of multicystic intra-abdominal lesion.
PET-Scan revealed a large ill-defined infiltrative mass lesion seen in relation to the abdominal mesentery, centred within the mesocolonic fat. The lesion measured 16 × 13.2 × 6.7 cm in size involving almost the entire abdominal cavity and demonstrate no significant contrast enhancement
Gross examination revealed a large multicystic mass with variable small size cysts measuring 17 × 10 × 4 cm in size. On serial sectioning, milky white fluid came out.
IHC for D240 positive in lining cells